목적: Parry Romberg Syndrome is a relatively rare congenital malformation that is difficult to treat and tends to be confused with Scleroderma or Craniofacial Cleft. Therefore, we conducted this study to share the clinical characteristics and treatment experience of PRS. 방법:We retrospectively analyzed 17 PRS patients who visited our hospital to analyze the clinical characteristics, DDx, treatment methods, side effects, and satisfaction. 결과:For the treatment of PRS, a composite graft was used in 1 case, and reconstructive rhinoplasty was performed using costal cartilage and forehead flap in all the others. Good results were obtained in most cases, but reoperation was required in 3 cases, and flap necrosis occurred in 1 case. There were 2 cases of dissatisfaction due to the small size of the flap. 결론:PRS is a rare congenital malformation that presents severe nasal asymmetry and tends to be confused with Scleroderma. Most of them required nasal reconstruction surgery using the forehead. Since nasal reconstruction surgery cannot completely satisfy patients, further research is needed to improve this.