Background: Low-grade fibromyxoid sarcoma (LGFMS) is a rare and indolent soft tissue sarcoma representing <5% of soft tissue sarcomas typically found in the deep soft tissues of the extremities and trunk. We present a case of a 68 year old male with an LGFMS in the larynx. This case highlights the diagnostic challenges posed by LGFMS in an atypical site and the importance of considering rare sarcomas in the differential diagnosis of laryngeal masses. Objective: This paper aims to report a case of a large LGFMS in a 68 year old male wherein diagnosis and treatment was delayed due to its uncommon location and its deceiving histologic features. Study Design: Case Report Setting: Tertiary Private Hospital Patient: This is a case of an elderly male with a 3-month history of dysphonia with a transglottic mass seen upon flexible nasopharyngolaryngoscopy. Because of impending upper airway obstruction, patient underwent Tracheostomy, Direct Laryngoscopy with Biopsy. Due to its malignant histologic features, patient underwent Total Laryngectomy with Frozen Section for margins of resection. Keywords: Fibromyxoid Sarcoma, Laryngeal mass, Vocal Cord Polyp, Spindle Cell Tumor, Case Report