Objectives: Kimura disease (KD) is a rare, chronic inflammatory disease of unknown cause characterized by painless subcutaneous swellings and lymphadenopathy commonly affecting the head and neck region. KD is usually confused for Angio lymphoid hyperplasia with eosinophilia and is associated with eosinophilia and increased serum IgE. Case: Our patient, a 44-year-old Mongolian male, the swelling was painless, pruritus. Due to severe itching in the left parotid area, with multiple red-pinkish bumps, scratches, and scars. Localized examination, a 3 cm × 4 cm was seen in the left parotid region. Facial asymmetry was maintained with normal facial nerve functions. Hematological examination revealed Neutrophils 31.1% and Eosinophils 36.6%. A contrast-enhanced computed tomography, which revealed multiple intra-parotid lymph nodes in the superficial lobe of the left parotid gland with an enlarged parotid gland but normal parotid parenchyma. The surgical specimen received consisted of brown-tan hardish tissue, measuring 5.2 x 3.5 x 2.5 cm. Many germinal centers of lymphoid follicles exhibited necrosis with protein debris, diffuse infiltration of eosinophils, and eosinophilic abscess formation. Based on those findings, the diagnosis of Kimura’s disease was confirmed. Conclusions: Kimura disease is a benign disease that mainly affects Asian men in their forties. KD should be included in the differential diagnosis and further explored. Histopathology is usually needed for a definitive diagnosis.