Rhabdomyosarcoma is the most common malignant tumor of the ear in children. We report a case of a 31-year old male with HIV presenting with a right external auditory canal mass which was determined to be a spindle-cell variant embryonal rhabdomyosarcoma. A 31-year old Filipino male presented with 3 months history of mild intermittent right ear pain accompanied by ear fullness, and yellowish non-foul smelling otorrhea. Unrecalled prescription otic drops relieved symptoms temporarily. 2 months prior to consultation, he developed progressive hearing loss, and bloody otorrhea during manipulation of the right ear. Consultation showed a fleshy mass in his right ear canal. Computed tomography revealed the mass extended into the middle ear. Biopsy and tissue staining resulted to a diagnosis of embryonal rhabdomyosarcoma, spindle-cell variant. Rhabdomyosarcoma is a primitive mesenchymal malignant tumor with a tendency for striated muscle tissue differentiation. In adults, the most common location in this age group is in the extremities. The most common histologic type is pleomorphic rhabdomyosarcoma which portends a worse prognosis compared to spindle cell embryonal rhabdomyosarcoma.