Alveolar soft part sarcoma (ASPS) is a rare soft tissue malignancy constituting less than 1% of soft tissue sarcoma. It primarily affects teenagers and young adults. Generally, ASPS grows slowly, but it is associated with a high incidence of metastasis, early in the course of the disease. Survival depends mostly on the presence of metastasis. It arises mostly in the extremities, especially the lower limbs. Approximately, one-fourth of the cases occur in the head and neck region and typical sites include the tongue and orbit, with other sites being very rare. In this case report, we present a case of ASPS encountered in the larynx with the review of literatures.