Relapsing polychondritis is an inflammatory disease that destroys systemic cartilage tissue. Though the pathogenenesis of the disease is not established yet, it is thought to be a kind of autoimmune disease. Inner ear symptoms such as sensorineural hearing loss and vertigo can be associated. A 42-year-old man who had been diagnosed with relapsing chondritis was admitted to our hospital with a symptom of acute vertigo. The patient showed direction-fixed left-beating horizontal nystagmus. Caloric test showed canal paresis on the right side, and B-MRI showed no abnormal finding. Under the diagnosis of acute peripheral vestibulopathy assoiated with relapsing polychondritis. He was treated with systemic steroid. 3 years later, the patient experienced 2nd vertigo attack. Right-beating spontaneous nystagmus was observed, and head impulse test showed catch-up saccade on both sides. Bilateral vestibulopathy could be diagnosed from the caloric test. B-MRI showed tiny vestibular schwannoma in the right internal auditory canal which had been missed in the previous MRI. This is, as far as we know, the first case report of tiny vestibular schwannoma in patient with relapsing polychondritis