Nasal extranodal natural killer/T cell (NK/T cell) lymphoma is relatively common in East Asia than in America, comprising up to 7-10% of all Non-Hodgkin’s lymphoma. Early nasal symptoms are nonspecific similar to chronic rhinosinusitis, such as nasal obstruction and nasal bleeding. With disease progression, inflammation and necrosis of the mucosa increase, hindering pathologic diagnosis. We experienced a case of nasal extranodal NK/T cell lymphoma in 58 year old woman who presented with recurrent periorbital swelling.