목적: The state of the auditory analyzer with hearing loss on The basis of consanguineous marriages. Identified functional features of the auditory analyzer in this pathology. 방법:Were subjected to a comprehensive survey of 50 young children with hearing loss on the basis of inbreeding: 30 boys (60%), 20 girls (40%). The presence of kinship parents established by anamnesis in children with hearing loss and their close relatives. To study the method used gaming tone threshold audiometry, otoacoustic emissions and ABR. 결과:When the game audiometry in young children is determined by the downward curve of the audiogram by type of sensorineural hearing loss. The results of the game audiometry in 50 children (3-5 years) showed the following: 18 (38%) is determined by the horizontal, in 21 (42%) horizontally - downward, and in 11 (22%) - precipitous configuration audiogram. When audiometric study the perception of sound by bone conduction in children of the first group with the horizontal and the second group with a horizontal configuration audiogram downward curve of bone conduction accompanied by a parallel configuration of the curve for air conduction audiogram. At the same time, the children of the third group with a steep curve audiogram configuration such patterns we observed. Further research conducted by recording the OAE and the ABR. These UAE 22% of children have shown a negative result, and when registering ABR fifth peak was registered at the intensity of the stimulation signal 70 dB. At the end of the game speech audiometry held in the Tajik language. All the children at the time of the study had the ability to voice communication with others. When the game speech audiometry all children surveyed showed 100% intelligibility. 결론:Thus, the results of hearing tests in infants showed the presence of sensorineural hearing loss on the basis of consanguineous marriages.